HOLT ORAM SYNDROME

For Students / PG Aspirants

Radial Club Hand

Radial Club Hand : *Longitudnal deficiency of radius *Mostly a bilateral deofrmity *Wrist is in marked radial deviation *Partial or whole of radius is absent *Thumb , scaphoid and trapezium might show diminished growth Syndromic Associations : 1. TAR Syndrome :  T – Thrombocytopenia AR – Absent Radius 2. HOLT ORAM SYNDROME : Fanconi’s anemia […]

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